Central Nervous System Tumors and Pseudo Tumors

CONDITION LINK TO THE CASES KNOW MORE AT A GLANCE
Non Neoplastic Masses
Lipoma 1 2 Know More At a glace
Focal cortical dysplasia 1 Know More At a glace
Hipothalamic Hamartoma 1 Know More At a glace
Abscess 1 2 Know More At a glace
Rathke’s Cleft Cyst 1 Know More At a glace
Choroid Plexus Hyperplasia 1 Know More At a glace
Langerhans Cell Histiocytosis 1 2 3 Know More At a glace
Castleman Disease 1 2 3 Know More At a glace
Foregut Duplication Cyst 1 Know More At a glace
Colloid Cyst 1 Know More At a glace
Choroid Plexus Cyst 1 Know More At a glace
Neuroglial Cyst 1 Know More At a glace
Neuroenteric Cyst 1 Know More
Hypothalamic Hamartoma 1 Know More At a glace
Pineal Gland Cyst 1 Know More At a glace
Tuberculoma 1 2 Know More At a glace
Tumefactive Demyelination 1 Know More
Phakomatosis
Ito Hypomelanosis 1
Basal Cell Nevus Syndrome (Gorlin Syndrome) 1
Encephalocraniocutaneous Lipomatosis 1
Neurofibromatosis Type 1 1 2
Neurofibromatosis Type 2 1 2
Tuberous Sclerosis Complex 1 2 3 4 5
Sturge-Weber Syndrome 1 2 3
Von Hippel-Lindau Disease 1 2
Ataxia-Telangiectasia 1
Incontinentia Pigmenti 1 2 3
Wyburn-Mason Syndrome
Klippel-Trenaunay Syndrome
Phakomatosis Pigmentovascularis
Neurocutaneous Melanosis 1
Parry-Romberg Syndrome 1
Cowden Syndrome (PTEN Hamartoma Tumor Syndrome)
Hereditary Hemorrhagic Telangiectasia (Osler-Weber-Rendu Syndrome) 1
Proteus Syndrome
Bannayan-Riley-Ruvalcaba Syndrome
Lhermitte-Duclos Disease (Dysplastic Gangliocytoma)
Schimmelpenning-Feuerstein-Mims Syndrome (Linear Nevus Sebaceous Syndrome)
Maffucci Syndrome
Blue Rubber Bleb Nevus Syndrome (Bean Syndrome)
Encephalocraniocutaneous Lipomatosis (Fishman Syndrome) 1
Gomez-Lopez-Hernandez Syndrome (Cerebello-trigeminal-dermal dysplasia)
McCune-Albright Syndrome 1
Noonan Syndrome with Multiple Lentigines (formerly LEOPARD Syndrome)
Waardenburg Syndrome
PHACE Syndrome 1
Piebaldism
Chediak-Higashi Syndrome
Griscelli Syndrome
Hermansky-Pudlak Syndrome
Sjogren-Larsson Syndrome
Menkes Disease (Kinky Hair Disease) 1 2 3 4 5
Xeroderma Pigmentosum
Gliomas, Glioneuronal Tumors, and Neuronal Tumors
Adult-type diffuse gliomas
Astrocytoma, IDH-mutant, grade 2 1 Know More At a Glance
Astrocytoma, IDH-mutant, grade 3 1 2 Know More At a Glance
Astrocytoma, IDH-mutant, grade 4 1
Oligodendroglioma, IDH-mutant and 1p/19q-codeleted, grade 2 1 Know More At a Glance
Oligodendroglioma, IDH-mutant and 1p/19q-codeleted, grade 3 1 Know More At a Glance
Glioblastoma, IDH-wildtype 1 2 3 Know More At a Glance
Pediatric-type diffuse low-grade gliomas
Diffuse astrocytoma, MYB- or MYBL1-altered
Angiocentric glioma 1 Know More At a Glance
Polymorphous low-grade neuroepithelial tumor of the young 1 2 Know More At a Glance
Diffuse low-grade glioma, MAPK pathway–altered
Pediatric-type diffuse high-grade gliomas
Diffuse midline glioma, H3 K27–altered 1 2 3 4 Know More At a Glance
Diffuse hemispheric glioma, H3 G34–mutant
Diffuse pediatric-type high-grade glioma, H3-wildtype and IDH-wildtype 1 2 Know More At a Glance
Infant-type hemispheric glioma
Circumscribed astrocytic gliomas
Pilomyxoid astrocytoma 1 2 3 4 5
Pilocytic astrocytoma 1 2 3 4 5 6 7 8 9 10 11 12 13 14 15 16 17 18 19 20 21 22 23 Know More At a Glance
High-grade astrocytoma with piloid features
Pleomorphic xanthoastrocytoma 1 2
Subependymal giant cell astrocytoma 1 2 3 Know More At a Glance
Chordoid glioma
Astroblastoma, MN1-altered 1 Know More At a Glance
Glioneuronal and neuronal tumors
Ganglioglioma 1 2 3 4 5 6 7 8 9 Know More At a Glance
Gangliocytoma 1 2
Desmoplastic infantile ganglioglioma 1 2 Know More At a Glance
Dysembryoplastic neuroepithelial tumor 1 2 3 4 Know More At a Glance
Diffuse glioneuronal tumor with oligodendroglioma-like features and nuclear clusters 1 2 3 Know More At a Glance
Papillary glioneuronal tumor 1 Know More At a Glance
Rosette-forming glioneuronal tumor 1 Know More At a Glance
Myxoid glioneuronal tumor 1 2 Know More At a Glance
Diffuse leptomeningeal glioneuronal tumor Know More At a Glance
Multinodular and vacuolating neuronal tumor 1 Know More At a Glance
Dysplastic cerebellar gangliocytoma (Lhermitte–Duclos disease)
Central neurocytoma 1 Know More At a Glance
Extraventricular neurocytoma
Cerebellar liponeurocytoma
Ependymal tumors
Supratentorial ependymoma, NOS 1 2 3 4 5 6 7 8 9 10
Supratentorial ependymoma, ZFTA fusion–positive
Supratentorial ependymoma, YAP1 fusion–positive
Posterior fossa ependymoma, NOS 1 2 3 4 5 6 7
Posterior fossa group A (PFA) ependymoma 1
Posterior fossa group B (PFB) ependymoma
Spinal ependymoma, NOSKnow More At a Glance
Spinal ependymoma, MYCN-amplified
Myxopapillary ependymoma1
Subependymoma 1 2 Know MoreAt a Glance
Choroid Plexus Tumors
Choroid Plexus Papilloma 1 2 3 4 5
Atypical choroid plexus papilloma 1 2
Choroid plexus carcinoma 1 2 3 4
Embryonal Tumors
Medulloblastomas, molecularly defined 1 2 3 4 5 6 7 8 9
Medulloblastoma, WNT-activated
Medulloblastoma, SHH-activated and TP53-wildtype
Medulloblastoma, SHH-activated and TP53-mutant
Medulloblastoma, non-WNT/non-SHH
Medulloblastomas, histologically defined
Medulloblastoma, histologically defined
Desmoplastic nodular medulloblastoma
Medulloblastoma with extensive nodularity
Large cell medulloblastoma
Anaplastic medulloblastoma
Other CNS embryonal tumors
Atypical teratoid/rhabdoid tumor 1 2 3 4 5 6 7
Cribriform neuroepithelial tumor (provisional entity)
Embryonal tumor with multilayered rosettes 1 2 3
CNS neuroblastoma, FOXR2-activated Know More At a Glance
CNS tumor with BCOR internal tandem duplication
CNS embryonal tumor, NEC/NOS
Pineal Tumors
Pineocytoma 1
Pineal parenchymal tumor of intermediate differentiation1
Pineoblastoma Know More At a glance
Papillary tumor of the pineal region
Desmoplastic myxoid tumor of the pineal region, SMARCB1-mutant (provisional entity)
Cranial and Paraspinal Nerve Tumors
Schwannoma
Neurofibroma
Plexiform neurofibroma
Perineurioma
Hybrid nerve sheath tumor
Malignant melanotic nerve sheath tumor
Malignant peripheral nerve sheath tumor
Cauda equina neuroendocrine tumor (previously paraganglioma)
Meningioma
Ganglioneuroblastoma 1
Mesenchymal, Non-Meningothelial Tumors Involving the CNS
Fibroblastic and myofibroblastic tumors
Solitary fibrous tumor 1
Vascular tumors
Cavernous hemangioma
Capillary hemangioma
Arteriovenous malformation
Hemangioblastoma 1 2 3
Cavernous sinus hemangioma1
Skeletal muscle tumors
Embryonal rhabdomyosarcoma
Alveolar rhabdomyosarcoma
Rhabdomyosarcoma, pleomorphic-type
Spindle cell rhabdomyosarcoma
Tumors of uncertain differentiation
Intracranial mesenchymal tumor, FET::CREB fusion–positive (provisional entity)
CIC-rearranged sarcoma
Primary intracranial sarcoma, DICER1-mutant
Ewing sarcoma 1 2 3 4 5
Chondrogenic tumors
Mesenchymal chondrosarcoma 1
Chondrosarcoma
Dedifferentiated chondrosarcoma
Notochordal tumors
Chordoma 1 2 3
Melanocytic Tumors
Diffuse meningeal melanocytic neoplasms
Meningeal melanocytosis
Meningeal melanomatosis
Circumscribed meningeal melanocytic neoplasms
Meningeal melanocytoma
Meningeal melanoma
Hematolymphoid Tumors Involving the CNS
CNS lymphomas
Primary diffuse large B-cell lymphoma of the CNS
Lymphomatoid granulomatosis (grades 1–3)
Intravascular large B-cell lymphoma
Miscellaneous rare lymphomas in the CNS
MALT lymphoma of the dura
Lymphoplasmacytic lymphoma
Follicular lymphoma
Anaplastic large cell lymphoma (ALK+/ALK–)
T-cell lymphoma
NK/T-cell lymphoma
Histiocytic tumors
Erdheim–Chester disease
Rosai–Dorfman disease
Juvenile xanthogranuloma
Langerhans cell histiocytosis
Histiocytic sarcoma
Germ Cell Tumors
Mature teratoma
Immature teratoma
Teratoma with somatic-type malignancy
Germinoma1 2 3
Embryonal carcinoma
Yolk sac tumor
Choriocarcinoma
Mixed germ cell tumor
Non germinomatous germ cell tumor 1
Tumors of the Sellar Region
Craniopharyngioma 1
Adamantinomatous craniopharyngioma 1 2 3 4
Papillary craniopharyngioma
Pituitaryoma
Granular cell tumor of the sellar region
Spindle cell oncocytoma
Pituitary adenoma / Pituitary neuroendocrine tumor (PitNET)
Cushing 1
Pituitary blastoma
Glial Neoplasm with ROS1 Fusion 1 Know More At a Glance